[Guillain-Barré syndrome with preserved reflexes].

Guillain-Barré is a rare, autoimmune disease of the peripheral nervous system. It can affect all ages beginning in the intrauterine or neonatal period. Clinical forms are diverse and include acute motor axonal neuropathy (AMAN). We report on a pediatric case of AMAN. A 2.5-year-old child presented with acute flaccid paralysis and preserved reflexes. Etiologic investigations argued in favor of Guillain-Barré syndrome in its AMAN form. Treatment based on IV immunoglobulins resulted in a total decline of paralysis and motor recovery. The AMAN form of Guillain-Barré syndrome should be considered as a potential diagnosis in all cases of acute flaccid paralysis with preserved reflexes.

Zouiri G ，Abilkassem R ，Zerhouni A ，Dini N ，Agadr A ... -  《-》

[Guillain-Barré syndrome in a child with normal tendon reflexes].

We describe the case of a 10-year-old child with the acute motor axonal neuropathy (AMAN) form of Guillain-Barré syndrome (GBS) with preserved tendon reflexes, 6 days after a bout of gastroenteritis. The child quickly showed weakness of the distal muscles of his four limbs, with preserved tendon reflexes and a raised CSF protein concentration with no cells. Nerve conduction studies showing motor axonal degeneration confirmed the diagnosis of GBS in spite of preserved tendon reflexes. The serum was positive for IgG antibodies to gangliosides GM1 and GD1b. The child received intravenous immunoglobulins, which resulted in a favorable progression. This case proves that GBS with normal tendon reflexes exists. The other cases of SGB with preserved tendon reflexes already described in the literature were the AMANs form with antibodies to gangliosides in the serum and only adults were affected.

Tellier S ，Gerdelat-Mas A ，Karsenty C ，Cancès C ，Tison C ，Chaix Y ，Cheuret E ... -  《-》

Role of IV Immunoglobulin in Indian Children With Guillain-Barré Syndrome.

Kalita J ，Kumar M ，Misra UK 《-》

Two unusual variants of Guillain-Barre syndrome.

Verma R ，Chaudhari TS 《-》

Clinical variants of Guillain-Barre syndrome: some aspects of differential diagnosis.

Dididze MN 《-》