Endovascular papillary angioendothelioma (Dabska tumor): underrecognized malignant tumor in childhood.

Endovascular papillary angioendothelioma, or Dabska tumor, was first presented in 1969 by Maria Dabska where she presented cases occurring in 6 children. The tumor was described as being a low-grade angiosarcoma characterized by papillary endovascular proliferations of atypical endothelial cells and anastomosing vascular channels within the dermis. Since its original description, only 30 case reports have been written describing the varying presentation, clinical course, and histopathology of this tumor. This case report documents the presentation and management of endovascular papillary angioendothelioma in a young male and reviews the current literature. Because more cases of EPAs are reported, perhaps a more standard approach to accurate diagnosis and treatment with surgical intervention and pathologic recognition via microscopy and immunohistochemistry can be determined.

Neves RI ，Stevenson J ，Hancey MJ ，Vangelisti G ，Miraliakbari R ，Mackay D ，Clarke L ... -  《-》

Endovascular papillary angioendothelioma in an elderly female.

Mishra A ，Tripathy K ，Bhuyan P ，Mohanty P ，Rath J ，Mohanty R ... -  《-》

The Dabska tumor: a thirty-year retrospect.

:The Dabska tumor is a rare low-grade angiosarcoma also known as malignant endovascular papillary angioendothelioma of childhood. It primarily affects the skin of children and has a distinctive histologic pattern of anastomosing vascular channels with intravascular papillary outpouchings projecting, sometimes, in a glomerulus-like pattern, into a lumen lined by atypical columnar endothelial cells. Since its original description 30 years ago by one of us, knowledge in this area has expanded.

Schwartz RA ，Dabski C ，Dabska M 《DERMATOLOGY》

Angiosarcoma arising within a Malignant Endovascular Papillary Angioendothelioma (Dabska tumor).

Antosz Z ，Zaniewski M ，Kostecki J ，Poreba R ... -  《-》

Papillary intralymphatic angioendothelioma of the thigh: A case report and review of the literature.

Ward KA ，Ecker PM ，White RR ，Melnik TE ，Gulbahce EH ，Wilke MS ，Sangueza OP ... -  《-》